Indian Journal of Pathology and Microbiology

CASE REPORT
Year
: 2015  |  Volume : 58  |  Issue : 4  |  Page : 531--533

Primary intracardiac malignant peripheral nerve sheath tumor: A rare case report


Sudheer Arava1, Saphalta Bagmar2, Parul Jain1, Muthu Kumaran3, Sanjeev Kumar4, Ruma Ray1 
1 Department of Pathology, All India Institute of Medical Sciences, New Delhi, India
2 Department of Medical Oncology, All India Institute of Medical Sciences, New Delhi, India
3 Department of Cardio-thoracic Surgery, All India Institute of Medical Sciences, New Delhi, India
4 Department of Cardiac Radiology, All India Institute of Medical Sciences, New Delhi, India

Correspondence Address:
Dr. Sudheer Arava
Department of Pathology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi - 110 029
India

Myxomas are the most common benign cardiac tumors constituting approximately 75% of all the cardiac tumors. Rest 25% are malignant and sarcomas being the commonest. Among the sarcomas primary cardiac malignant peripheral nerve sheath tumors are extremely rare. They usually arise in relation to the branches of vagus or phrenic nerves, 5-42% being associated with neurofibromatosis type 1. Clinical signs and symptoms depend on the location and extent of involvement. Complete resection is the treatment of choice but local recurrence is common.


How to cite this article:
Arava S, Bagmar S, Jain P, Kumaran M, Kumar S, Ray R. Primary intracardiac malignant peripheral nerve sheath tumor: A rare case report.Indian J Pathol Microbiol 2015;58:531-533


How to cite this URL:
Arava S, Bagmar S, Jain P, Kumaran M, Kumar S, Ray R. Primary intracardiac malignant peripheral nerve sheath tumor: A rare case report. Indian J Pathol Microbiol [serial online] 2015 [cited 2020 Aug 4 ];58:531-533
Available from: http://www.ijpmonline.org/article.asp?issn=0377-4929;year=2015;volume=58;issue=4;spage=531;epage=533;aulast=Arava;type=0