Indian Journal of Pathology and Microbiology

CLINICO-PATHOLOGY CONFERENCE
Year
: 2016  |  Volume : 59  |  Issue : 3  |  Page : 339--347

Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease


KP Srikanth1, Inusha Panigrahi2, Babu Ram Thapa1, Kim Vaiphei3 
1 Department of Pediatric Gastroenterology, Postgraduate Institute of Medical Education and Research, Chandigarh, India
2 Advanced Pediatric Centre, Postgraduate Institute of Medical Education and Research, Chandigarh, India
3 Department of Histopathology, Postgraduate Institute of Medical Education and Research, Chandigarh, India

Correspondence Address:
Prof. Kim Vaiphei
Department of Histopathology, Postgraduate Institute of Medical Education and Research, Chandigarh - 160 012
India

We present a rare presentation of cystic fibrosis with neonatal cholestasis. Histological features of mucoviscidosis were present in liver involving the biliary tract, intestinal mucosa, pancreas, and lung. Besides, there was a rare association with autosomal dominant type of polycystic renal disease.


How to cite this article:
Srikanth K P, Panigrahi I, Thapa BR, Vaiphei K. Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease.Indian J Pathol Microbiol 2016;59:339-347


How to cite this URL:
Srikanth K P, Panigrahi I, Thapa BR, Vaiphei K. Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease. Indian J Pathol Microbiol [serial online] 2016 [cited 2020 Jan 29 ];59:339-347
Available from: http://www.ijpmonline.org/article.asp?issn=0377-4929;year=2016;volume=59;issue=3;spage=339;epage=347;aulast=Srikanth;type=0