Indian Journal of Pathology and Microbiology

CASE REPORT
Year
: 2013  |  Volume : 56  |  Issue : 4  |  Page : 396--398

Dumb-bell shaped poorly differentiated pelvic synovial sarcoma with molecular confirmation: A rare presentation of an uncommon disease entity


Roumina Hasan1, Sandeep Kumar2, Lakshmi Rao1 
1 Department of Pathology, Kasturba Medical College, Manipal University, Manipal, Karnataka, India
2 Department of Radiodiagnosis, Kasturba Medical College, Manipal University, Manipal, Karnataka, India

Correspondence Address:
Roumina Hasan
Departments of Pathology, Kasturba Medical College, Manipal University, Manipal, Karnataka
India

Pelvic localization of synovial sarcoma is a rare phenomenon and to the best of our knowledge its presentation as a large DQdumb-bellDQ-shaped abdomino-pelvic mass showing extension to the thigh has never been reported in the literature. We report a case of a young adult presenting with retention of urine and was found to have a large abdomino-pelvic mass causing bony destruction and compression of pelvic viscera. A biopsy revealed a cellular tumor composed of spindle to oval cells arranged in a hemangiopericytomatous pattern. Histopathology was suggestive of poorly differentiated synovial sarcoma. Immunohistochemistry (IHC) was positive for vimentin, CD 99, Bcl2, Mic2 and focally for EMA and negative for CD 34, CK, desmin, synaptophysin, and WT1. Due to equivocal IHC findings molecular analysis was done which confirmed the diagnosis as synovial sarcoma.


How to cite this article:
Hasan R, Kumar S, Rao L. Dumb-bell shaped poorly differentiated pelvic synovial sarcoma with molecular confirmation: A rare presentation of an uncommon disease entity.Indian J Pathol Microbiol 2013;56:396-398


How to cite this URL:
Hasan R, Kumar S, Rao L. Dumb-bell shaped poorly differentiated pelvic synovial sarcoma with molecular confirmation: A rare presentation of an uncommon disease entity. Indian J Pathol Microbiol [serial online] 2013 [cited 2020 Oct 24 ];56:396-398
Available from: https://www.ijpmonline.org/article.asp?issn=0377-4929;year=2013;volume=56;issue=4;spage=396;epage=398;aulast=Hasan;type=0