Indian Journal of Pathology and Microbiology

CASE REPORT
Year
: 2017  |  Volume : 60  |  Issue : 3  |  Page : 399--401

Intrapulmonary ectopic liver associated with scimitar syndrome


Sajna V. M. Kutty1, M Lilly1, Shalini Kuruvila1, Sajan Koshy2 
1 Department of Pathology, Aster Malabar Institute of Medical Sciences, Kozhikode, Kerala, India
2 Department of Pathology, Aster Malabar Institute of Medical Sciences, Kozhikode, Kerala; Department of Cardiac Sciences, Aster Medcity, Kochi, Kerala, India

Correspondence Address:
Sajna V. M. Kutty
Department of Pathology, Old Block, 2nd Floor, Aster Malabar Institute of Medical Sciences, P. O. Govindapuram, Kozhikode - 673 016, Kerala
India

We report a case of intrapulmonary ectopic liver associated with Scimitar syndrome. A two month old male child who presented with features of congestive cardiac failure underwent extensive cardiac and radiological investigations and was diagnosed with Scimitar syndrome. He was also found to have a mass in the lower lobe of the right lung, the possibilities being either a pulmonary sequestration or a diaphragmatic hernia. As his dyspnea progressively worsened, a right lower lobectomy was performed at the age of two years. Intraoperatively, no connecting pedicle or hernia sac was seen. The resected lung specimen showed a light brown mass enclosed by the lung parenchyma and microscopy showed cords of normal hepatocytes with portal tracts. The hepatocytes were positive for Hep Par1, and bile ducts were CK 7 positive. To the best of our knowledge, this is the first reported case of an intrapulmonary ectopic liver associated with Scimitar syndrome.


How to cite this article:
Kutty SV, Lilly M, Kuruvila S, Koshy S. Intrapulmonary ectopic liver associated with scimitar syndrome.Indian J Pathol Microbiol 2017;60:399-401


How to cite this URL:
Kutty SV, Lilly M, Kuruvila S, Koshy S. Intrapulmonary ectopic liver associated with scimitar syndrome. Indian J Pathol Microbiol [serial online] 2017 [cited 2021 Sep 21 ];60:399-401
Available from: https://www.ijpmonline.org/article.asp?issn=0377-4929;year=2017;volume=60;issue=3;spage=399;epage=401;aulast=Kutty;type=0