Indian Journal of Pathology and Microbiology

: 2018  |  Volume : 61  |  Issue : 3  |  Page : 450--451

A rare case of accessory mitral valve tissue

Kim Vaiphei1, Rajesh Kumar1, Ajay Bahl2,  
1 Department of Histopathology, Post Graduate Institute of Medical Education and Research, Chandigarh, India
2 Department of Cardiology, Post Graduate Institute of Medical Education and Research, Chandigarh, India

Correspondence Address:
Kim Vaiphei
Department of Histopathology, Post Graduate Institute of Medical Education and Research, Chandigarh - 160 012

How to cite this article:
Vaiphei K, Kumar R, Bahl A. A rare case of accessory mitral valve tissue.Indian J Pathol Microbiol 2018;61:450-451

How to cite this URL:
Vaiphei K, Kumar R, Bahl A. A rare case of accessory mitral valve tissue. Indian J Pathol Microbiol [serial online] 2018 [cited 2021 Jan 27 ];61:450-451
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Full Text

A 49-years-old male, an uptopsy case, who wasen symptomatic for 15 –years, presented to the cardiology outpatient door with the history of breathlessness (New York Heart Association Class II) and palpitation on exertion with occasional nonanginal chest pain. He also complained of occasional episodes of syncope. Echocardiography revealed features of hypertrophic cardiomyopathy with interventricular septum thickening measuring 26 mm, left ventricular ejection fraction of 77%, and systolic anterior motion. He also had evidence of mild mitral regurgitation with left atrial size of 54 mm. During the course of the disease, he had worsening of symptoms with orthopnea, elevated jugular venous pressure, and a palpable liver 1 cm below right costal margin. He developed further complications and presented in the emergency with features of atrial fibrillation with fast ventricular rate and congestive heart failure. He sustained cardiac arrest, from which he could not be revived. At autopsy (consented by the next of kin), the heart was grossly overweight weighing 460 g with concentric biventricular hypertrophy and cavity dilatation. All valves were normal except the mitral valve with a well-defined accessory mitral valve tissue (AMVT) along the left outflow, attached firmly to left ventricular wall just beneath the left coronary and noncoronary aortic valves [Figure 1]. This accessory leaflet was in continuity with the native mitral valve, having multiple minor and one major chordae tendineae attached to anterior papillary muscle. Histology of the section taken along the left ventricular outflow tract showed a membranous tissue firmly adherent to the underlying left ventricular cardiac myocytes, except the inferior most portion of the accessory valve tissue [Figure 2].{Figure 1}{Figure 2}

AMVT is a rare congenital malformation diagnosed usually in childhood and may occur in isolation or along with other cardiac malformations.[1] It may remain asymptomatic or cause left ventricular outflow obstruction.[2],[3] Surgical excision and correction of the associated anomalies are the treatment of choice.[4] The indexed case is a rare variant of membranous type of AMVT which was undiagnosed during life, reemphasizing the importance of routine autopsy in documentation of such type of rare congenital anomaly.

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The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

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